When we compared the results of the SLC26A4 testing in Tuvinian patients with their GJB2 genotypes, four patients with the SLC26A4-related HL were also the carriers of one pathogenic GJB2 allele and two patients were coincidently GJB2- and SLC26A4-heterozygotes. The gene discussed is GJB2; the disease is Hodgkins lymphoma.