Epithelioid schwannoma and epithelioid malignant peripheral nerve sheath tumor (MPNST) lie in the differential as well, but they are consistently negative for melanocytic markers including MITF, and a subset of them shows loss of INI1 expression [42,43]. The gene discussed is SMARCB1; the disease is Epithelioid Malignant Peripheral Nerve Sheath Tumor.