We report here a PMC arising from a Pancreatic Intraductal Papillary Mucinous Neoplasm (IPMN), both having KRAS and TP53 mutations.<h4>Case presentation</h4>We report the case of a 73-year-old woman presenting with right iliac fossa pain. This evidence concerns the gene KRAS and paramyotonia congenita of Von Eulenburg.