EATL type 2, in contrast, is characterized by a monomorphic infiltration of small- to medium-sized T-lymphocytes CD3+, CD4−, CD8+, CD56+, and TCR α/β+ [85,86], and is typically not associated with CeD, suggesting a different pathogenetic mechanism compared to type 1. Here, CD8A is linked to cranioectodermal dysplasia.