Though GJB2 is the most common mutation worldwide in different populations, other important genes include SLC26A4, GJB3, GJB6, MYO15A, MYO7A, TMC1, CDH23 etc. were also identified in the pathogenesis of NSHL [24–28]. The gene discussed is GJB3; the disease is nodular sclerosis classical Hodgkin lymphoma.