SMARCB1 and rhabdoid tumor: Like extracranial malignant rhabdoid tumours, ATRT is genetically characterized by homozygous inactivating mutations in the SWItch/Sucrose Non-Fermentable (SWI/SNF)-related, Matrix-associated, actin-dependent Regulator of Chromatin, subfamily B, member 1 (SMARCB1) gene, or less frequently SMARCA4, which encode core subunits of the SWI/SNF chromatin remodelling complex [3].