Of particular interest and rather new among these NEN mimickers are tumors from the Ewing Sarcomas group, desmoplastic small round cell tumors, epithelioid neoplasms with FUS-CREM gene fusions, epithelioid sarcomas, synovial sarcomas, SMARCA4- and SMARCB1-deficient neoplasms (Fig. 6), clear cell sarcomas of the gastrointestinal tract, alveolar soft part sarcomas, solitary fibrous tumors, chordomas, melanomas, and sclerosing epithelioid mesenchymal neoplasms. Here, SMARCB1 is linked to Ewing sarcoma.