To date, SMARCB1 loss has been described in about 100 sinonasal carcinomas worldwide, mostly among SNUC, and a worse outcome has been demonstrated in these cases, while more rarely, this alteration was observed in NKSCC and in tumors with plasmacytoid and rhabdoid morphologies [14,15,16,17]. Here, SMARCB1 is linked to nasal cavity and paranasal sinus carcinoma.