Indeed, molecularly distinct subtypes of sinonasal carcinomas, including SMARCB1-INI1 or SMARCA4 deficient sinonasal carcinoma, isocitrate dehydrogenase (IDH)-mutant SNUC, ARID1A mutant PDSNCs, and NUT carcinomas (harboring NUT-variant fusions), have recently been proposed as separate entities [2,9,10,11]. The gene discussed is IDH2; the disease is nut midline carcinoma.