Specifically, plasma ADAMTS13 levels were lower in PAH patients compared to CTEPH (p < 0.0001), HFpEF-PH (p < 0.0001), HFrEF-PH (p < 0.0001), Dyspnoea/HF-non-PH (p < 0.0001) as well as healthy controls (p = 0.0055) (Figure 1(a) and (d)). Here, ADAMTS13 is linked to pulmonary arterial hypertension.