Desmoplastic small round cell tumor (DSRCT), a rare and aggressive STS that is characterized by translocation between EWSR1 and WT1, is typically treated with intensive multimodal therapy including alkylator-based chemotherapy, cytoreductive surgery with or without hyperthermic intraperitoneal chemotherapy (HIPEC), and whole abdominopelvic radiotherapy (82). Here, WT1 is linked to desmoplastic small round cell tumor.