Prior to the characterization of PPB-like peritoneal sarcoma as a distinct entity, Warren et al reported two cases in 5-year old and 16-year old girls who presented with a right adnexal mass and a pelvic mass with omental and peritoneal metastases, respectively; these two cases as pointed out by the authors had pathologic features of types II/III PPB; both cases had a somatic DICER1 mutation in addition to a germline mutation in one case which was the only one tested79. The gene discussed is DICER1; the disease is pleuropulmonary blastoma.