It is unclear at this time whether there is an association between DICER1 mutated thyroid teratomas and DICER1 predisposition tumor syndrome since to our knowledge no cases of cervicothyroidal teratomas have been reported in DICER1 kindreds or in association with other DICER1 related tumors in the experience of the IPPBR. The gene discussed is DICER1; the disease is BAP1-related tumor predisposition syndrome.