In our study, one novel WNT10A gene mutation causing oligodontia was identified, expanding the WNT10A mutation spectrum, and our analyses identified several new correlations: maxillary and mandibular molar agenesis is most often associated with PAX9 mutations, maxillary lateral incisor, and mandibular incisors agenesis is most linked to EDA mutations, and mandibular first premolar agenesis is least associated with PAX9 mutations. The gene discussed is PAX9; the disease is Oligodontia.