There are two main clinicopathological variants: SPD that presents as superficial pustules particularly on the intertriginous areas, subcorneal neutrophilic pustules, and IgA deposition in the upper epidermal ICS; and IEND presenting as sunflower-like inflammatory pustules, diffuse intraepidermal neutrophilic infiltrates, and IgA deposition involving all epidermal ICS. Here, CD79A is linked to Platelet storage pool disease.