KCNH2 and familial long QT syndrome: While inherited forms are relatively rare, with an estimated prevalence of ~1:2,000 of apparently healthy newborns (8, 10), acquired LQTS is a quite frequent finding (11, 12), more commonly due to medications blocking the human ether-à-go-go related gene K+ channel (hERG-K+) carrying the rapidly activating component of the delayed outward-rectifying current (IKr), or electrolyte imbalances (hypokalaemia, hypocalcaemia, hypomagnesemia) (1, 9).