Screening renal ultrasound, MRI, or urinalysis for renal cell carcinoma could also be considered (21), as these patients are prone to renal cell carcinoma and BAP1 mutated renal tumors appear to grow at a faster rate than kidney cancers driven by other mutations such as in von Hippel-Lindau disease (19). The gene discussed is BAP1; the disease is hereditary clear cell renal cell carcinoma.