We suggest that some morphological and immunophenotypical features, including diverse architectural patterns, compactly aggregated small tubules, glands containing intraluminal hyaline-like eosinophilic secretions, and variable degrees of PAX2 and GATA3 staining may be designated as MLD in association with common histological subtypes of endometrial carcinoma. Here, PAX2 is linked to metachromatic leukodystrophy.