High levels of CCN2/CTGF has been reported in skeletal muscle biopsies from Duchenne muscular dystrophy (DMD), Becker muscular dystrophy, and Fukuyama-type congenital muscular dystrophy patients [31,46], and in samples from murine models for DMD and Limb-Girdle muscular dystrophy (LGMD) [30,32,47]. Here, CCN2 is linked to Becker muscular dystrophy.