SLC26A4 is not the only gene present within the CEVA haplotype, which also spans BCAP29, COG5, DUS4L, HBP1, PIK3CG, and PRKAR2B. For none of these genes, pathogenic variants associated with (syndromic) HL have been reported, nor has a function in the inner ear been described. The gene discussed is PRKAR2B; the disease is Hodgkins lymphoma.