HNF1B and gout: Its multi-organ expression results in a wide spectrum of renal and extra-renal manifestations in patients with HNF1B-associated disease, which includes renal cysts, multicystic dysplastic kidney, solitary kidney, agenesis of pancreas body and tail, maturity-onset diabetes in the young type 5, genital malformations, elevated liver enzymes, electrolyte abnormalities, primary hyperparathyroidism, gout, and epilepsy [4,5].