In neoplasms with pleomorphic and/or rhabdoid morphology such as SMARCB1-deficient neoplasms, SMARCA4-deficient neoplasms, malignant SFT, and CCS, a diagnosis of large cell NEC was proposed, while a NET diagnosis was discussed in the chordoma case and two of the CCSs. The gene discussed is SMARCA4; the disease is chordoma.