Adenomatous polyposis coli (APC)-associated polyposis, PTEN hamartoma tumor syndrome, Peutz-Jeghers syndrome, Carney’s complex, and DICER1 are syndromic forms of FNMTC that follow an autosomal dominant mode of inheritance, whereas Werner’s syndrome, Pendred syndrome, and ataxia telangiectasia are autosomal recessive types of syndromic FNMTCs (1). This evidence concerns the gene APC and PTEN hamartoma tumor syndrome.