HNF1B and autosomal dominant medullary cystic kidney disease with or without hyperuricemia: In other renal conditions, however, such as autosomal-dominant tubulointerstitial kidney disease (ADTKD), a new disease classification was successfully established, combining the mode of inheritance, major clinical manifestation, and underlying genetic defect in one term (ADTKD-UMOD; ADTKD-REN, ADTKD-MUC1, and ADTKD-HNF1B) (Bleyer et al., 2017).