Overt cranial nerve manifestation is only occasionally seen in NF155+ CIDP, although its frequency seems to be somewhat higher in NF155+ CIDP than in NF155− CIDP (5, 32): visual disturbance [23.1% (3/13) vs. 7.3% (3/41)], facial sensory disturbance [23.1% (3/13) vs. 17.1% (7/41)], and facial palsy [15.4% (2/13) vs. 4.9% (2/41)] (5). Here, PMP22 is linked to Facial palsy.