Coenzyme Q8B (OMIM * 615567) glomerular nephropathy (COQ8B-GN) or nephrotic syndrome type 9 (NPHS9, OMIM # 615573) is an autosomal recessive type of CKD, inherited through allelic homogeneous variant or compound heterozygous variants. This evidence concerns the gene COQ8B and familial idiopathic steroid-resistant nephrotic syndrome.