Despite their phenotypic differences, achondrogenesis type IA (Smits et al., 2010; ACG1A; MIM 200600) and odontochondrodysplasia (Wehrle et al., 2019; ODCD; MIM 184260) are both caused by mutations of thyroid hormone receptor interactor 11 (TRIP11), which encodes the Golgi-associated microtubule-binding protein 210 (GMAP-210). Here, TRIP11 is linked to odontochondrodysplasia.