GJB2 and deafness: In addition to OTOF-related deafness, mutations in the autosomal genes like CDH23, Claudin14, GJB2, GJB6, MYO6, MYO15A, SLC26A4, TMC1, TMIE, TMPRSS3, TRIOBP, USHIC, and others are predominant to cause HHL among Indian and Pakistani populations (Yan et al., 2015).