Further, LSD1 was described as critical for neuronal progenitor cell (NPC) maintenance during cortical development, controlling NPC differentiation by regulating H3K4 methylation of ATN1 (encoding Atrophin 1, a protein related to dentatorubral-pallidoluysian atrophy) [113]. Here, ATN1 is linked to Dentatorubral pallidoluysian atrophy.