Some genes, including ABCC8 (106), GCK (107), INS (108), KCNJ11 (109), and PDX1 (110) may alternatively cause PNMD or MODY, with various severity and clinical features depending on the gene, nature of the mutation, and genotype (homozygous or heterozygous). This evidence concerns the gene KCNJ11 and MODY.