PDX1 and MODY: In addition, rare MODY cases [accounting for up to 6% of all MODY forms (49)] have been diagnosed with mutations in PDX1 (59), HNF1B (60), NEUROD1 (61, 62), KLF11 (63), CEL (64), PAX4 (65), INS (66), BLK (67), ABCC8 (68), KCNJ11 (69), and APPL1 (70) (known as MODY4-14).