Similar clinical phenotypes that present in patients affected by ABCA4-linked autosomal recessive Stargardt disease (STGD1) can also be observed in ELOVL4-linked autosomal dominant Stargardt disease (STGD3) [13,14], in PROM1-linked autosomal dominant Stargardt disease (STGD4) [15], and in an autosomal dominant macular dystrophy associated with a c.422A>G p.(Tyr141Cys) PRPH2 variant [16]. This evidence concerns the gene PRPH2 and Stargardt disease 3.