FGG and ornithine translocase deficiency: However, only eight fibrinogen gamma chain mutations: Brescia (Gly384Arg), Aguadilla (Arg375Trp), Al du Pont Thr314Pro), Angers G316_Q350del), Beograd (Gly336Ser), Pisa (Asp316Asn), Ankara (His340Asp), Trabzon 8Thr371Ile) [89] and a single mutation on the A alpha chain (c.103C > T) [91] have been proven to result in hepatic storage and in a new disease, called hereditary hypofibrinogenemia with hepatic storage (HHHS) [1,15,16].