1.1. Idiopathic1.2. Heritable1.2.1 BMPR2 mutation1.2.2 Other mutations1.3. Drugs and toxins induced1.4. Associated with:1.4.1. Connective tissue disease1.4.2. Human immunodeficiency virus (HIV) infection1.4.3. Portal hypertension1.4.4. Congenital heart disease1.4.5. Schistosomiasis1.5 PAH long-term responders to calcium channel blockers1.6 PAH with overt features of venous/capillaries (PVOD/PCH) involvement1.7 Persistent PH of the newborn syndrome. The gene discussed is BMPR2; the disease is pulmonary arterial hypertension.