Although Taiwan was the first country to report an intense association of human leukocyte antigen (HLA)-B*15:02 and carbamazepine-induced SJS/TEN (6), and the first to implement HLA-B*15:02 screening for carbamazepine users (7), reports focusing on ocular manifestations of SJS/TEN from Taiwan are limited. The gene discussed is HLA-B; the disease is Schwartz-Jampel syndrome.