Iron overload was regularly detected in hepatocytes of DGUOK mutant patients by liver histological examination.[4] Thus, we checked the expression of seven genes (TF, TFRC, DMT1, FPN, IRP1, IRP2, HAMP) in iron metabolism in control, patient and corrected iHep and iHep‐Orgs. Here, ACO1 is linked to Tangier disease.