FKRP and autosomal recessive limb-girdle muscular dystrophy type 2I: To undertake these analyses, two distinct FKRP-deficient patient myoblast cell lines from either end of the FKRP clinical spectrum were differentiated to form myotubes: those derived from a patient with LGMD2I, a disease with a milder clinical presentation, and cells derived from a patient with a severe CMD.