CHCHD2 mutations are associated with the spectrum of LBDs (Funayama et al., 2015), while CHCHD10 mutations are associated with the spectrum of FTD-ALS and mitochondrial myopathies (Bannwarth et al., 2014; Johnson et al., 2014; Müller et al., 2014; Ajroud-Driss et al., 2015; Zhang et al., 2015; Genin et al., 2016; Rubino et al., 2018). Here, CHCHD10 is linked to Mitochondrial myopathy.