The cardiac event rate in diagnosed patients over a median follow-up of 31.9 (14 to 54.4) months has been reported to be 5% overall, which increased to 7.7% in patients with aborted SCD, while family history of SCD or the presence of an SCN5A mutation were not predictive of arrhythmic events [2]. This evidence concerns the gene SCN5A and Schnyder corneal dystrophy.