Finally, MTVSs had a higher rate of NF syndrome (commonly NF2) compared with spinal MPNSTs (commonly NF1) (18.5% vs. 14.0%), and NF2 patients with a malignant transformation of a vestibular schwannoma may have a poorer prognosis compared to NF1 patients with spinal MPNST (50). Here, NF2 is linked to malignant peripheral nerve sheath tumor.