A high frequency of aKIRs, KIR3DS1, 2DS1, and 2DS5 and a low frequency of an iKIR of KIR3DL1 were observed in Japanese patients with VKH disease compared with healthy controls (42.2% vs 21.4% and 76.9% vs 98.8%, respectively) (100). This evidence concerns the gene KIR3DL1 and Vogt-Koyanagi-Harada disease.