It is known that the typical three megabase deletion that accounts for 85% of cases includes complete deletion of LZTR1. 8 Yet no single case of schwannoma appears in 3,054 reports of Di George syndrome on PubMed (searches using the terms: Di George syndrome AND “schwannoma” and 22q11.2 deletion syndrome AND “schwannoma” were carried out at https://pubmed.ncbi.nlm.nih.gov/?term=Di+George+syndrome+&sort=date, 22 September 2020), nor in 3,031 reports of 22q11.2 deletion syndrome. Here, LZTR1 is linked to schwannoma.