Although clinical characteristics of KD and MISC partly overlap, we think our case’s diagnosis was recurrent KD instead of MISC because epidemiological (male, 3 y old with a previous history of KD treated with IVIG), clinical (no abdominal pain, none of MISC-typical echocardiographic findings) and laboratory features (normal AST/ALT, LDH, pro-BNP and ferritin, no lymphopenia) were suggestive of KD rather than MISC. The gene discussed is GPT; the disease is lymphopenia.