A thorough review, including 57 articles, showed that the assertion of ARVC causality was initially derived from 3 publications from the same research group who first established linkage to chromosome 1q42-43, and subsequently to RYR2 in families with a phenotype called arrhythmogenic right ventricular dysplasia 2 described as CPVT with fibro-fatty replacement of the right ventricle.42 The clinical features described in these manuscripts reflect CPVT rather than ARVC with cases not meeting TFC. This evidence concerns the gene RYR2 and catecholaminergic polymorphic ventricular tachycardia.