On the molecular level, lipoblastomas typically show a rearrangement of the chromosomal region 8q11–13, which results most commonly in a fusion of the pleomorphic adenoma gene 1 (PLAG1) with diverse partners, most commonly HAS2 (8q24.1) and COL1A2 (7q22) [9, 10]. The gene discussed is PLAG1; the disease is lipoblastoma.