Of note, some patients with PID associated with autoinflammation may be initially referred to rheumatologists for complaints supportive of SLE or Behçet disease (as in the case of STAT1 GOF, A20 haploinsufficiency syndromes, WDR1 deficiency), and infective symptoms may be misinterpreted as a complication of immunosuppressive treatments [117]. Here, STAT1 is linked to systemic lupus erythematosus.