ADA and hyperinsulinemic hypoglycemia, familial, 4: Here, thymic alymphoplasia [30], immunoglobulin A deficiency [31], GATA2 deficiency (MonoMac disease) [32] and adenosine deaminase-deficient severe combined immunodeficiency (ADA-SCID) [33] are inherited diseases that have been observed as drivers of secondary PAP.