FH type I (FH-I) or glucocorticoid remediable hyperaldosteronism (GRA) is the result of aldosterone overproduction due to ACTH-dependent activation of aldosterone synthase and was initially described in 1966 in a single family, with identification of the causative chimeric gene 26 years later (11, 12). The gene discussed is POMC; the disease is glucocorticoid-remediable aldosteronism.