VHL and malignant epithelioid mesothelioma: Deletion occurs in approximately 25% of peritoneal MM.[14]BAP1 (BRCA-associated protein 1) mutations or deletions, however, can occur in up to 80% of epithelioid mesothelioma cases.[15] Smith-Hannah et al reported VHL gene mutation in clear cell peritoneal epithelioid mesothelioma.[11] We also identified VHL gene alteration involving exon 1.