Compared with the general population, patients with NF1 in our study had significantly higher rates of pheochromocytoma (OR, 126; 95% CI, 81-195; P < .0001) and NET (OR, 14.1; 95% CI, 7.3-21.1; P < .0001). Here, NF1 is linked to hereditary pheochromocytoma-paraganglioma.