As Tubastatin A could restore TDP‐43 pathology and has been reported to rescue axonal transport deficits in neurodegenerative diseases, including ALS (Guo et al, 2017), we explored the effect of Tubastatin A on the axonal transport defects present in the mutant TDP43 iPSC‐derived motor neurons. This evidence concerns the gene TARDBP and amyotrophic lateral sclerosis.