The spontaneous occurrence and clinical similarity of these lesions to human neurofibromatosis could make them a valuable animal model to study genetic predisposition to cancer, but more research is needed to classify the genetic, molecular, and pathological basis of PNST in these animals and how they relate to NF1, NF2, and schwannomatosis in order to determine their effective use as comparative disease models. Here, NF2 is linked to schwannomatosis.