Dilated cardiomyopathy with ataxia (DCMA, 3-methylglutaconic aciduria, type V) is an autosomal recessive disorder caused by loss of DNAJC19, an IMM protein thought to facilitate CL remodeling by TAZ, which is associated with changes in CL acyl chain composition, albeit not total CL levels [122,123]. The gene discussed is DNAJC19; the disease is 3-methylglutaconic aciduria type 5.